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OPA1

OPA,即视神经萎缩蛋白1,别名OpticAtrophyType1。它是由人类OPA1基因编码的蛋白,主要在线粒体内膜上发挥作用。OPA1的作用机制包括调控线粒体的融合过程,维持线粒体形态和功能,以及参与线粒体呼吸链超级复合物的组装和线粒体嵴的重塑。OPA1对维持细胞能量代谢、细胞死亡、增殖以及基因表达调控具有重要作用。OPA1的异常与多种疾病相关,尤其是与视神经萎缩(ADOA)和更广泛的神经系统症状。

热销产品

OPA1 Antibody (CSB-PA016340LA01HU)

验证数据

CSB-PA016340LA01HU

Western Blot
Positive WB detected in: Hela whole cell lysate, MCF-7 whole cell lysate, HepG2 whole cell lysate, K562 whole cell lysate, Mouse heart tissue
All lanes: OPA1 antibody at 1:2000
Secondary
Goat polyclonal to rabbit IgG at 1/50000 dilution
Predicted band size: 112, 116 kDa
Observed band size: 112 kDa

OPA1 Antibodies

OPA1 for Homo sapiens (Human)

OPA1 Proteins

OPA1 Proteins for Homo sapiens (Human)