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ATXN3

ATXN3,即Ataxin-3,别名A7LFZ5、ATX3、D6RDL9、E9PB63、MJD1、SCA3等。ATXN3由人类ATXN3基因编码,该基因位于染色体14q32.1上。ATXN3在蛋白质质量控制和降解中发挥重要作用,通过去泛素化作用参与蛋白质的降解和蛋白质聚集的调控。ATXN3在神经退行性疾病中扮演着重要角色,特别是在SCA3中。ATXN3的突变可能导致蛋白质聚集和神经细胞功能障碍。ATXN3的功能失常可能导致神经元健康问题和其他神经退行性疾病,在这些疾病中,ATXN3的异常调控可能影响神经细胞的存活和功能。

热销产品

ATXN3 Antibody (CSB-PA002443LA01HU)

验证数据

CSB-PA002443LA01HU

Western blot
All lanes: ATXN3 antibody at 2µg/ml
Lane 1: 293T whole cell lysate
Lane 2: Mouse brain tissue
Lane 3: MCF-7 whole cell lysate
Secondary
Goat polyclonal to rabbit IgG at 1/10000 dilution
Predicted band size: 42, 36, 40, 21 kDa
Observed band size: 42 kDa

CSB-PA002443LA01HU

Immunohistochemistry of paraffin-embedded human lung cancer using CSB-PA002443LA01HU at dilution of 1:100

CSB-PA002443LA01HU

Immunohistochemistry of paraffin-embedded human pancreatic tissue using CSB-PA002443LA01HU at dilution of 1:100

ATXN3 Antibodies

ATXN3 for Homo sapiens (Human)

ATXN3 Proteins

ATXN3 Proteins for Homo sapiens (Human)

ATXN3 Proteins for Rattus norvegicus (Rat)

ATXN3 Proteins for Mus musculus (Mouse)

ATXN3 Proteins for Gallus gallus (Chicken)