ATXN3
ATXN3,即Ataxin-3,别名A7LFZ5、ATX3、D6RDL9、E9PB63、MJD1、SCA3等。ATXN3由人类ATXN3基因编码,该基因位于染色体14q32.1上。ATXN3在蛋白质质量控制和降解中发挥重要作用,通过去泛素化作用参与蛋白质的降解和蛋白质聚集的调控。ATXN3在神经退行性疾病中扮演着重要角色,特别是在SCA3中。ATXN3的突变可能导致蛋白质聚集和神经细胞功能障碍。ATXN3的功能失常可能导致神经元健康问题和其他神经退行性疾病,在这些疾病中,ATXN3的异常调控可能影响神经细胞的存活和功能。
热销产品
ATXN3 Antibody (CSB-PA002443LA01HU)
验证数据

Western blot
All lanes: ATXN3 antibody at 2µg/ml
Lane 1: 293T whole cell lysate
Lane 2: Mouse brain tissue
Lane 3: MCF-7 whole cell lysate
Secondary
Goat polyclonal to rabbit IgG at 1/10000 dilution
Predicted band size: 42, 36, 40, 21 kDa
Observed band size: 42 kDa

Immunohistochemistry of paraffin-embedded human lung cancer using CSB-PA002443LA01HU at dilution of 1:100

Immunohistochemistry of paraffin-embedded human pancreatic tissue using CSB-PA002443LA01HU at dilution of 1:100
ATXN3 Antibodies
ATXN3 for Homo sapiens (Human)
产品货号 | 产品名称 | 种属反应性 | 应用类型 |
---|---|---|---|
CSB-PA002443GA01HU | ATXN3 Antibody | Human,Mouse,Rat | ELISA,WB,IHC |
CSB-PA002443LA01HU | ATXN3 Antibody | Human, Mouse | ELISA, WB, IHC |
ATXN3 Proteins
ATXN3 Proteins for Homo sapiens (Human)
产品货号 | 产品名称 | 来源 |
---|---|---|
CSB-YP002443HU CSB-BP002443HU CSB-MP002443HU CSB-EP002443HU-B |
Recombinant Human Ataxin-3 (ATXN3) | Yeast Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
CSB-EP002443HU | Recombinant Human Ataxin-3 (ATXN3) | E.coli |
ATXN3 Proteins for Rattus norvegicus (Rat)
产品货号 | 产品名称 | 来源 |
---|---|---|
CSB-YP002443RA CSB-EP002443RA CSB-BP002443RA CSB-MP002443RA CSB-EP002443RA-B |
Recombinant Rat Ataxin-3 (Atxn3) | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |
ATXN3 Proteins for Mus musculus (Mouse)
产品货号 | 产品名称 | 来源 |
---|---|---|
CSB-YP863445MO CSB-BP863445MO CSB-EP863445MO-B |
Recombinant Mouse Ataxin-3 (Atxn3) | Yeast Baculovirus In Vivo Biotinylation in E.coli |
ATXN3 Proteins for Gallus gallus (Chicken)
产品货号 | 产品名称 | 来源 |
---|---|---|
CSB-YP894318CH CSB-EP894318CH CSB-BP894318CH CSB-MP894318CH CSB-EP894318CH-B |
Recombinant Chicken Ataxin-3 (ATXN3) | Yeast E.coli Baculovirus Mammalian cell In Vivo Biotinylation in E.coli |