PET100 Antibody, FITC conjugated

产品详情

产品名称：

Rabbit anti-Homo sapiens (Human) PET100 Polyclonal antibody
Uniprot No.：

P0DJ07
基因名：

PET100
别名：

mitochondrial antibody; PET100 antibody; Protein PET100 homolog antibody; PT100_HUMAN antibody
宿主：

Rabbit
反应种属：

Human
免疫原：

Recombinant Human Protein PET100 homolog, mitochondrial protein (26-73AA)
免疫原种属：

Homo sapiens (Human)
标记方式：

FITC
克隆类型：

Polyclonal
抗体亚型：

IgG
纯化方式：

>95%, Protein G purified
浓度：

It differs from different batches. Please contact us to confirm it.
保存缓冲液：

Preservative: 0.03% Proclin 300
Constituents: 50% Glycerol, 0.01M PBS, PH 7.4
产品提供形式：

Liquid
储存条件：

Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
货期：

Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
用途：

For Research Use Only. Not for use in diagnostic or therapeutic procedures.

功能：

Plays an essential role in mitochondrial complex IV maturation and assembly.
基因功能参考文献：
1. The short isoform of the myofibrillogenesis regulator 1 (MR-1S) as a new COX assembly factor, which works with the highly conserved PET100 and PET117 chaperones to assist COX biogenesis in higher eukaryotes. PMID: 28199844
2. We identify PET100 as a complex IV biogenesis factor in humans and characterize its location and role in mitochondria.We found PET100 (MIM 614770) mutations in ten Lebanese individuals with Leigh syndrome and isolated complex IV deficiency. PMID: 24462369
3. Protein identified in mammalian mitochondria PMID: 22356826
4. COX assembly candidate, ortholog of fungal PET100 PMID: 22356826
亚细胞定位：

Membrane; Single-pass membrane protein. Mitochondrion. Mitochondrion inner membrane.
蛋白家族：

PET100 family
数据库链接：

HGNC: 40038

OMIM: 614770

KEGG: hsa:100131801

STRING: 9606.ENSP00000470539

UniGene: Hs.728837