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中文名称：
ALG9兔多克隆抗体
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货号：
CSB-PA131441
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规格：
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图片：
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The image on the left is immunohistochemistry of paraffin-embedded Human brain tissue using CSB-PA131441(ALG9 Antibody) at dilution 1/60, on the right is treated with fusion protein. (Original magnification: ×200)
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The image on the left is immunohistochemistry of paraffin-embedded Human thyroid cancer tissue using CSB-PA131441(ALG9 Antibody) at dilution 1/60, on the right is treated with fusion protein. (Original magnification: ×200)
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Gel: 8%SDS-PAGE, Lysate: 40 μg, Lane: Human fetal liver tissue, Primary antibody: CSB-PA131441(ALG9 Antibody) at dilution 1/200 dilution, Secondary antibody: Goat anti rabbit IgG at 1/8000 dilution, Exposure time: 1 minute
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其他：
产品详情
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Uniprot No.：
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基因名：
ALG9
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别名：
ALG9 antibody; ALG9_HUMAN antibody; Alpha-1,2-mannosyltransferase ALG9 antibody; Asparagine-linked glycosylation protein 9 homolog antibody; Disrupted in bipolar disorder protein 1 antibody
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宿主：
Rabbit
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反应种属：
Human,Mouse
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免疫原：
Fusion protein of Human ALG9
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免疫原种属：
Homo sapiens (Human)
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标记方式：
Non-conjugated
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抗体亚型：
IgG
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纯化方式：
Antigen affinity purification
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浓度：
It differs from different batches. Please contact us to confirm it.
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保存缓冲液：
-20°C, pH7.4 PBS, 0.05% NaN3, 40% Glycerol
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产品提供形式：
Liquid
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应用范围：
ELISA,WB,IHC
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推荐稀释比：
| Application |
Recommended Dilution |
| ELISA |
1:1000-1:2000 |
| WB |
1:200-1:1000 |
| IHC |
1:50-1:200 |
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Protocols：
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储存条件：
Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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货期：
Basically, we can dispatch the products out in 1-3 working days after receiving your orders. Delivery time maybe differs from different purchasing way or location, please kindly consult your local distributors for specific delivery time.
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用途：
For Research Use Only. Not for use in diagnostic or therapeutic procedures.
靶点详情
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功能：
Catalyzes the transfer of mannose from Dol-P-Man to lipid-linked oligosaccharides.
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基因功能参考文献：
- ALG9 is upregulated in peripheral blood mononuclear cells of galactosaemia patients. PMID: 26733289
- Our study shows that some pathogenic variants in ALG9 can present as a lethal skeletal dysplasia with visceral malformations as the most severe phenotype PMID: 25966638
- Due to the ALG9 deficiency, cells accumulated the lipid-linked oligosaccharides Man(6)GlcNAc(2)-PP-dolichol and Man(8)GlcNAc(2)-PP-dolichol. PMID: 19451548
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相关疾病：
Congenital disorder of glycosylation 1L (CDG1L); Gillessen-Kaesbach-Nishimura syndrome (GIKANIS)
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亚细胞定位：
Endoplasmic reticulum membrane; Multi-pass membrane protein.
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蛋白家族：
Glycosyltransferase 22 family
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组织特异性：
Ubiquitously expressed; with highest levels in heart, liver and pancreas.
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数据库链接：
Most popular with customers
The image on the left is immunohistochemistry of paraffin-embedded Human brain tissue using CSB-PA131441(ALG9 Antibody) at dilution 1/60, on the right is treated with fusion protein. (Original magnification: ×200)
The image on the left is immunohistochemistry of paraffin-embedded Human thyroid cancer tissue using CSB-PA131441(ALG9 Antibody) at dilution 1/60, on the right is treated with fusion protein. (Original magnification: ×200)
Gel: 8%SDS-PAGE, Lysate: 40 μg, Lane: Human fetal liver tissue, Primary antibody: CSB-PA131441(ALG9 Antibody) at dilution 1/200 dilution, Secondary antibody: Goat anti rabbit IgG at 1/8000 dilution, Exposure time: 1 minute
